Esferocitosis hereditaria. Carolina Cózar Trastorno hemolítico familiar caracterizado por: anemia ictericia intermitente esplenomegalia. Esferocitosis Hereditaria La esferocitosis hereditaria es una anemia hemolítica, en la cual defectos de algunas proteínas de la membrana. Esferocitosis hereditaria. Revisión. Parte II. Manifestaciones clínicas, evolución, complicaciones y tratamiento. PUBLISHED | A. Posadas.
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Download PDF Cite this paper. Hereditary spherocytosis must always be suspected in children with anemia, hyperbilirubinem ia, splenomegaly or cholelithiasis, in the asymptomatic individual with an affected relative, and in the neonate with hyperbilirubinemia with no blood group incompatibility; its early detection is key to avoid kernicterus.
Follow-up of these patients is based on periodical control and supply of information on the adequate management of hemolytic or aplastic crisis, and early detection of cholelithiasis.
The decision esferocitosiw perform splenectomy is usually associated with quality of life rather than life-threatening risk, and it should result from a consensus between patient, parents and physicians. The postsplenectomy follow-up is based on control of compliance with the prophylactic antibiotic therapy and the early diagnosis of infectious disorders.
A Iolascon 16 Estimated H-index: Natural history of hereditary spherocytosis during the first year of life. Disorders of the Red Cell Membrane. Jean Delaunay 37 Estimated H-index: Guidelines for the diagnosis and management of hereditary spherocytosis — update.
Esferocitosis by Juan Carlos Zepeda on Prezi
Bolton-Maggs 12 Estimated H-index: Replication of the B19 parvovirus in human bone marrow cell cultures. K Ozawa 1 Estimated H-index: Gilbert syndrome increasing unconjugated hyperbilirubinemia in a child with hereditary spherocytosis.
Dipti Kumar 6 Estimated H-index: Abnormalities of the erythrocyte membrane. Gallagher 39 Estimated H-index: Successful recombinant erythropoietin therapy for a developing anemic newborn with hereditary spherocytosis.
Shigeharu Hosono 16 Estimated H-index: Serum erythropoietin levels during infancy: Kling 11 Estimated H-index: The morbidity and mortality of pediatric splenectomy: Martin Jugenburg 1 Estimated H-index: Are you looking for